Superior Semicircular Canal Dehiscence Syndrome in a Woman: A Case Report

Abstract

Background: Superior semicircular canal dehiscence (SSCD) syndrome is a disease that occurs very
rare. Clinical presentation consists of Tullio’s phenomenon and Hennebert’s sign. This case presentation
is atypical and clinician should be aware. Purpose: to present the rare case of Superior semicircular canal
dehisence (SSCD) Case presentation: A 65-year-old woman with complaints of dizziness from 2 years ago
and her recurrence. The audiogram showed bilateral sensorineural deafness with a mean hearing threshold
of 58 decibels (dB) of the right ear and 48 dB of the left ear. There is also an air-bone gap in the right ear
at low frequencies (250 Hz). The tympanogram revealed a type A result in both ears. Positive results were
obtained on the examination of Romberg sharpened, positive Fukuda step to the right, and the Gans test. CT
scan showed dehiscence of the right superior semicircular canal. Therapy in patients was given conservative
therapy because the participants refused to undergo surgery. Conclusion: SSCD has a specific symptom of
Tullio’s phenomenon and CT scan shows dehiscence of the superior semicircular canal.