Reduction Surgery of Giant Hemifacial Neurofibromas: A Case Report

Authors

  • Ruby Riana A
  • Sitti Rizaliyana
  • Radias Dwi Padmani
  • Retno Handajani
  • S. Perdanakusuma

DOI:

https://doi.org/10.37506/ijfmt.v16i1.17628

Keywords:

Giant facial neurofibromas, benign tumour, neurofibromatosis type 1, surgical reduction

Abstract

Neurofibromatosis type 1 (NF-1), first described by Von Recklinghausen (1882), is an autosomal dominant disease caused by a spectrum of mutations in NF-1 gene. We reported a case of giant facial neurofibromas in 26 years old male patient without family history of neurofibromatosis type 1. Features typical of neurofibroma, including an enlarged nerve fascicle composed of elongated nuclei and scant cytoplasmic cells, were identified. Excision was performed with preservation of parotid duct. The mass weight was about 5,5 kg. There were some challenges during the procedure, such as bleeding, hypovolemia, and preservation of vital structure.

Author Biographies

Ruby Riana A

Researcher, Doctoral Study Program, Faculty of Medicine Universitas Airlangga, Surabaya, Jawa Timur, Indonesia,Lecturer, Surgery Department, Faculty of Medicine Universitas Muhammadiyah Malang, Malang, East Java, Indonesia

Sitti Rizaliyana

Lecturer, Plastic Reconstructive & Aesthetic Surgery Department, Faculty of Medicine Universitas Airlangga,Indonesia.

Radias Dwi Padmani

Lecturer, Surgery Department, Faculty of Medicine Universitas Nahdlatul Ulama Surabaya, Surabaya, East Java, Indonesia.

Retno Handajani

Professor, Department of Medical Biochemistry, Faculty of Medicine Universitas Airlangga, Surabaya, East Java, Indonesia, Plastic Reconstructive & Aesthetic Surgery Department, Faculty of Medicine,Indonesia

S. Perdanakusuma

Professor, Universitas Airlangga, Dr. Soetomo Academic General Hospital, Surabaya, East Java, Indonesia

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Published

2021-11-30

How to Cite

Ruby Riana A, Sitti Rizaliyana, Radias Dwi Padmani, Retno Handajani, & S. Perdanakusuma. (2021). Reduction Surgery of Giant Hemifacial Neurofibromas: A Case Report. Indian Journal of Forensic Medicine & Toxicology, 16(1), 1017–1020. https://doi.org/10.37506/ijfmt.v16i1.17628