Pleural Effusion in Limited Cutaneous Systemic Sclerosis : A Report

Abstract

Systemic sclerosis (SSc) is a chronic autoimmune multisystem disorder characterized by endothelial
dysfunction and fibroblast dysfunction, which results in progressive fibrosis of the skin and internal
organs more frequently the lungs and gastro intestinal tract. Pulmonary involvement is common in the
course of SSc, with Interstitial Lung Disease (ILD) and Pulmonary Arterial Hypertension (PAH) along
with pleural effusion being the leading causes of death. Here we report, case of an elderly male patient
presenting with cutaneous SSc with multiple uncommon pulmonary manifestations like ILD with right
sided pleural effusion with hepatic cyst.